Telecanthus

Telecanthus, or dystopia canthorum, refers to increased distance between the inner corners of the eyelids (medial canthi), while the inter-pupillary distance is normal. This is in contrast to hypertelorism, in which the distance between the whole eyes is increased.[1] Telecanthus and hypertelorism are each associated with multiple congenital disorders.

Diagram showing the definition of telecanthus, or dystopia canthorum

The distance between the inner corners of the eyelids is called the intercanthal distance. In most people, the intercanthal distance is equal to the width of each eye (the distance between the inner and outer corners of each eye). The average interpupillary distance is 60–62 millimeters (mm), which corresponds to an intercanthal distance of approximately 30–31 mm.[2]

Traumatic telecanthus refers to telcanthus resulting from traumatic injury to the nasal-orbital-ethmoid (NOE) complex.[1] The diagnosis of traumatic telecanthus requires a measurement in excess of those normative values. The pathology can be either unilateral or bilateral, with the former more difficult to measure.[2]

Systemic associations

Telecanthus is often associated with many congenital disorders. Congenital disorders such as Down syndrome, fetal alcohol syndrome, cri du chat syndrome, Klinefelter syndrome, Turner syndrome, Ehlers–Danlos syndrome, Waardenburg syndrome[3] often present with prominent epicanthal folds, and if these folds are nasal (most commonly are) they will cause telecanthus.

Etymology

Telecanthus comes from the Greek word τῆλε (tele, "far") and the Latin word canthus, meaning corner of the eyelid. Dystopia canthorum comes from the Greek δυσ- (dus-, “bad”) and τόπος (tópos, “place”) and the Latin word canthorum ("of the canthi").

See also
  • Blepharophimosis, reduced size of the eyelid openings, which can result in telecanthus

References
  1. "Telecanthus - EyeWiki". eyewiki.aao.org. Retrieved 2019-12-07.
  2. "Resident Manual of Trauma to the Face, Head, and Neck, Ed. 1" (PDF). Retrieved 12 January 2015.
  3. Tagra S, Talwar AK, Walia RL, Sidhu P (2006). "Waardenburg syndrome". Indian J Dermatol Venereol Leprol. 72 (4): 326. doi:10.4103/0378-6323.26718. PMID 16880590.
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